Introduction -- Anatomy of Tetralogy of Fallot -- Genetics -- Stem Cells and the Right Ventricle -- Pathophysiology in Tetralogy of Fallot -- Tetralogy of Fallot: Late Outcome -- Tetralogy of Fallot: the Failing Right Ventricle.-Imaging Evaluation -- Timing for RVOT Management -- Percutaneous Pulmonary Valve.-Other Transcatheter Procedures.- Surgical Pulmonary Valve Implantation -- Other Surgical Procedures -- Late Arrhythmias: Current Approaches -- Perioperative Right Ventricular Management.         .

Tetralogy of Fallot is the most common form of cyanotic congenital heart disease, and one of the first to be successfully repaired by congenital heart surgeons. Although “fixed”, patients born with tetralogy of Fallot cannot be considered “cured”. Improving survival and quality of life for this ever-increasing adult population will continue to challenge the current and future generations of cardiologists. Adult patients with tetralogy of Fallot should be seen by a cardiologist specializing in the care of adults with congenital heart disease, to be monitored for late complications. They need to be checked regularly for any subsequent complications or disturbances of heart rhythm. This monograph is intended as both an introduction to the subject and a timely, comprehensive review, and will be welcomed by adult cardiologists, pediatric cardiologists, internists, surgeons, obstetricians, and intensivists who wish to learn about the most recent discoveries and advances concerning tetralogy of Fallot in adults. It will also be of interest to advanced undergraduates wanting to learn more about the subject.